Pediatric Mixed Functioning Adrenocortical Carcinoma: A Case Report and Review of Literature

نویسندگان
Jha, Chandan Kumar ID 1
Mishra, Saroj Kanta ID 2
Verma, Ritu ID 3
Krishna, Abhishek ID 4
Yadav, Sanjay ID 5

1 Department of General Surgery, All India Institute of Medical Sciences, Patna, India

2 Department of Endocrine Surgery, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

3 Department of Pathology, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

4 Department of Endocrine Surgery, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

5 Department of Endocrine Surgery, Sanjay Gandhi PG Inst. of Medical Sciences, Lucknow, India

doi
10.30476/mejc.2019.78633.
چکیده

Adrenocortical carcinoma (ACC) is a very rare disease in the pediatric age group. The clinic-biological profile, histopathological criteria of diagnosis, and staging of this disease in this age group are different from those of adult ACC. In this paper, we report a case of pediatric ACC presenting as Cushing syndrome that was managed with complete surgical excision. Through this case presentation, we highlight the sequential protocol of investigations and management in a child suspected of having ACC.

کلیدواژه‌ها
Pediatric ACC, Cushing’s syndrome