Pachydermodactyly: A Rare Type of Macrodactyly as a Dermatological Sign of Compulsive Behavior and Repetitive Minor Trauma; a Case Report and Review of the Literature
نویسندگان
1 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
2 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
3 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia
4 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
5 State University of Novi Pazar, Department of Psychology, Novi Pazar, Republic of Serbia
6 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
7 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
8 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia
9 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
10 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia
11 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
12 Faculty of Medicine, University of Novi Sad, Novi Sad, Republic of Serbia Institute for Children and Youth Health Care of Vojvodina, Novi Sad, Republic of Serbia
13 Health Center, Temerin, Republic of Serbia
doi
10.5812/ircmj.79992.چکیده
Introduction: Pachydermodactyly is a very rare type of macrodactyly. It clinically resembles juvenile rheumatoid arthritis, but it has a non-inflammatory etiology without bone, articular, or synovial involvement.Case Presentation: In this study, we report the case of a 15-year-old boy with repetitive behavior diagnosed with a pachyder- modactyly after evaluation of bilateral swelling of the proximal interphalangeal joints. Histologic examination revealed epider- mal hyperorthokeratosis, thickening of the dermis with increased dermal collagen and absence of inflammatory cells. Pachyder- modactyly is a very rare condition associated with compulsive behavior and results from repetitive minor trauma that causes local- ized proliferation of fibrous tissue. Conclusions: Pachydermodactyly is a dermatological sign of compulsive behavior and repetitive minor trauma, and it should bedistinguished from other forms of joint enlargement to avoid unnecessary medicamentous treatment. Control examinations did not reveal clinically relevant worsening even without any treatment applied.