فهرست نشریات علمی دسترسی آزاد ایران

Introduction: Urinary tract infection is a common disease in the general population. However, in patients with frequent urinary tract infection, it is important todetermine any treatable cause to avoid recurrence.Case Presentation: Herlyn-Werner-Wunderlich syndrome or OHVIRA syndrome is a very rare congenital anomaly with uterus didelphys, obstructed hemivagina, andipsilateral renal agenesis. The earliest presentation of this syndrome is hematocolpos that develops during menstruation and results in dysmenorrhea and a pelvic massshortly after menarche. Herein, we report a patient with Herlyn-Werner-Wunderlich syndrome manifested with unusual symptoms, delayed onset and without surgery.The unique point of this patient is the partial obstruction of cervico-vaginal junction.Conclusions: Early diagnosis and timely treatment of OHVIRA syndrome can prevent long-term complications, such as recurrent urinary tract infection and infertility.A high index of suspicion is required, even though OHVIRA syndrome is extremely rare and may have an atypical presentation.