Congenital Insensitivity to Pain with Anhidrosis (CIPA): A Case Report
نویسندگان
1 Department of Prosthodontic, Faculty of Dentistry, Shiraz University of Medical Sciences, Shiraz, Iran
2 Department of Prosthodontic, Faculty of Dentistry, Shiraz University of Medical Sciences, Shiraz, Iran
3 Department of Prosthodontic, Faculty of Dentistry, Shiraz University of Medical Sciences, Shiraz, Iran
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چکیده
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disorder characterized by episodes of fever andthe inability to sense of pain despite the fact that all other sensory modalities remain intact or minimally impaired.The patient also may exhibit the signs of self-mutilation, mental retardation and little or no perspiration. We presenta 10 years old Iranian patient diagnosed with CIPA with the above-mentioned clinical characteristics. Theprosthetic treatment and the subsequent six month follow-up are discussed. Follow-up of the patient revealedthat, with the use of this prosthesis, the patient’s oral function and esthetics were established and the mouthlesions improved. Therefore especial dental management of CIPA patients according to their mental status, age,oral and dental condition is essential for solving the specific problems each case may present and the full mouthteeth extraction should be considered as the last treatment.