Pediatric Adrenocortical Carcinoma: Diagnostic Challenges and Therapeutic Approach — A Case Report
نویسندگان
1 Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria - Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria
2 Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria - Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria
doi
10.18502/ijpho.v15i4.19637چکیده
Adrenocortical carcinoma (ACC) is a rare tumor. It constitutes 0.2% of malignant tumors in children and it is considered ten times rarer than in adults. Patients with predisposing syndromes like Li-Fraumeni or Beckwith-Wiedemann may develop these tumors. Clinical symptoms are dominated by endocrine signs, which are present in 90% of cases. ...